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Jaundice in the newborn

SNOMED: 276549000702 wordsUpdated 03/03/2026
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Exam Tips

  • In OSCEs, explicitly state that visual inspection cannot quantify bilirubin severity; confirm with serum bilirubin and age-specific treatment thresholds.
  • Jaundice in first 24 hours is pathological until proven otherwise and needs urgent paediatric/neonatal assessment.
  • Ask directly about stool and urine colour: pale stools + dark urine strongly suggest conjugated jaundice/cholestasis.
  • Remember prevalence figures: around 60% of term and 80% of preterm babies are jaundiced in week 1.
  • Use red-flag neuro signs (poor suck, high-pitched cry, abnormal tone/opisthotonus, seizures) to identify possible acute bilirubin encephalopathy quickly.
  • For viva illustration of cephalocaudal spread and stool-colour warning signs, refer to standard neonatal examination diagrams and stool-colour charts used in UK newborn care materials.

Definition

Neonatal jaundice is yellow discoloration of a newborn’s skin and sclera caused by hyperbilirubinaemia from bilirubin accumulation. It is very common in the first week of life and is usually physiological, but early-onset (<24 hours), rapidly rising, prolonged, or conjugated jaundice can indicate serious disease and risk bilirubin neurotoxicity.

Pathophysiology

Neonates produce more bilirubin than adults because they have a higher red cell mass and shorter red cell lifespan. Haem breakdown generates unconjugated bilirubin, which is albumin-bound in plasma; immature hepatic uptake/conjugation (UGT activity) and increased enterohepatic circulation make early neonatal unconjugated hyperbilirubinaemia common. If unconjugated bilirubin rises markedly, unbound bilirubin can cross the blood-brain barrier (especially with prematurity, sepsis, hypoxia, acidosis, or low albumin) and cause acute bilirubin encephalopathy/kernicterus. Conjugated hyperbilirubinaemia suggests hepatobiliary pathology (for example biliary atresia, neonatal hepatitis, metabolic disease) rather than physiological jaundice.

Risk Factors

  • Prematurity (lower gestational age)
  • Low birth weight
  • Jaundice appearing in first 24 hours
  • Previous sibling/parental history of neonatal jaundice needing treatment
  • Exclusive breastfeeding with suboptimal intake
  • Dehydration or excessive postnatal weight loss
  • Bruising/cephalhaematoma or birth trauma
  • Maternal age >25 years
  • East Asian or Mediterranean ethnicity
  • Infant of diabetic mother (especially macrosomic infant)
  • Family history of haemolytic disorders including G6PD deficiency
  • Down syndrome

Clinical Features

Symptoms

  • Parental concern about yellow skin or yellow eyes
  • Poor feeding or reduced effective milk transfer
  • Reduced wet/dirty nappies suggesting poor intake
  • Dark urine and/or pale, chalky stools (red flag for cholestasis)
  • Lethargy, irritability, fever, vomiting, or apnoeic episodes in unwell infant

Signs

  • Cephalocaudal progression of jaundice (head then trunk/limbs with increasing severity)
  • Visible jaundice in sclerae, gums, and blanched skin (harder to detect in darker skin)
  • Fever or other signs of sepsis
  • Dehydration and significant weight loss
  • Bruising/cephalhaematoma
  • Neurological signs of acute bilirubin encephalopathy: poor suck, altered tone, opisthotonus, high-pitched cry, seizures, coma

Investigations

Total serum bilirubin (TSB), age-specific nomogram assessment:Confirms degree of hyperbilirubinaemia; do not estimate severity by visual inspection alone
Fractionated bilirubin (conjugated/direct and unconjugated/indirect):Predominantly unconjugated pattern in physiological jaundice; raised conjugated bilirubin suggests cholestatic/hepatobiliary disease
Maternal and neonatal blood group, Rh status, direct antiglobulin test (DAT):Supports haemolytic disease due to ABO/Rh incompatibility
Full blood count, reticulocyte count, blood film:Anaemia/reticulocytosis or haemolytic changes suggest haemolysis
Sepsis work-up (CRP, blood culture ± urine/cerebrospinal fluid as indicated):Identifies infective cause in unwell neonate
Liver panel and clotting profile:Abnormal liver enzymes/synthetic function support hepatobiliary pathology
Thyroid function tests:Detects congenital hypothyroidism in prolonged jaundice
G6PD assay (timed appropriately):Enzyme deficiency supports inherited haemolytic jaundice risk
Metabolic tests (for example galactosaemia screen) when prolonged/unwell:Abnormal results indicate inborn error/metabolic liver disease
Stool and urine colour assessment:Pale stools and dark urine are red flags for conjugated jaundice (for example biliary atresia)

Management

Lifestyle Modifications

  • Urgent same-day assessment for jaundice in first 24 hours, rapidly worsening jaundice, or any unwell infant
  • Support effective feeding (breastfeeding/formula support), monitor weight and hydration, and track nappies
  • Provide parents with safety-net advice: seek urgent care for poor feeding, lethargy, fever, arching/high-pitched cry, dark urine, or pale stools
  • Do not use sunlight exposure as treatment because of unreliable efficacy and safety concerns
  • Document jaundice assessment at each neonatal contact, especially first 72 hours

Pharmacological Treatment

Immunoglobulin for immune haemolysis

  • Human normal immunoglobulin (IVIG) 500 mg/kg IV over 4 hours; may repeat once after 12 hours in specialist neonatal care

Used when isoimmune haemolytic disease is driving severe/rising unconjugated bilirubin despite intensive phototherapy. Monitor for infusion reactions, haemolysis, thrombosis, renal impairment, and fluid overload; use neonatal specialist protocol.

Surgical / Interventional

  • Exchange transfusion for severe hyperbilirubinaemia at/above treatment thresholds or with signs of acute bilirubin encephalopathy despite intensive phototherapy
  • Cause-specific procedures when indicated, for example Kasai portoenterostomy for biliary atresia

Complications

  • Acute bilirubin encephalopathy
  • Kernicterus (clinical-pathological syndrome of bilirubin neurotoxicity)
  • Chronic bilirubin encephalopathy with choreoathetoid cerebral palsy
  • Sensorineural hearing impairment
  • Developmental delay, learning and visual problems
  • Seizures and permanent neurological disability

Prognosis

Most neonatal jaundice is physiological and resolves spontaneously (typically by about 2 weeks in term infants; longer in preterm infants). Prolonged unconjugated jaundice in a well baby is often benign and self-limiting, but outcomes depend on rapid recognition of severe hyperbilirubinaemia and underlying causes; timely phototherapy/escalation prevents most bilirubin toxicity.

Sources & References

NICE Guidelines(1)

📖Textbook References(2)

  • [Oxford Medical Handbooks] Ian Wilkinson, Tim Raine, Kate Wiles, Anna Goodhart, Catriona Ha - Oxford Handbook of Clinical Medicine (2017, Oxford University Press) - libgen.li.pdf(pp. 287)[context]
  • [Oxford Medical Handbooks] Ian Wilkinson, Tim Raine, Kate Wiles, Anna Goodhart, Catriona Ha - Oxford Handbook of Clinical Medicine (2017, Oxford University Press) - libgen.li.pdf(pp. 286, 287)[context]

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